Idiopathic Pulmonary Fibrosis and Progressive Pulmonary Fibrosis in Adults
Introduction
Introduction
- Progress in the diagnosis and treatment of idiopathic pulmonary fibrosis (IPF) and other interstitial lung diseases (ILDs) manifesting progressive pulmonary fibrosis (PPF) has generated the need for updating guidelines.
- These recommendations are not mandates because they cannot account for all unique clinical circumstances and should be revisited as new evidence is published.
Recommendations
...ommendations...
...I. Update on the Diagnosis and Treat...
...nsbronchial lung cryobiopsy (TBLC) be regarded a...
...ommendation for or against the add...
...not treating patients with IPF with antacid...
...ot referring patients with IPF for a...
Part II. Diagnosis and Treatment of PPF...
...irfenido...
...recommend further research into the...
Nintedani...
...ntedanib for the treatment of PPF in patien...
We recommend research into the efficacy, ef...
Tables
Tabl...
...resolution Computed Tomography (HRCT) Pat...
Table 2. Definition of PPFHaving t...
.... Selected Fibrotic Lung Diseases Tha...
Figures
...gures...
...gure 1. IPF Diagnosis Based Upon HRCT an...
...gure 2. Diagnostic Algorithm for IPFa...
Figure 3. Schematic Pathway for Clinical Managemen...
...ILD Manifesting PPFa The committee acknowledges...
...Traction Bronchiectasis/bronchiolectasisAxial,...
...oneycombingAxial, sagittal, and cor...
...ure 7. Paraseptal EmphysemaAxial and coronal CT im...
...irspace Enlargement With Fibrosis (AE...
...9. Spectrum of CT Appearances in UIP Patt...
...attern Due to Connective Disease CTD-UIP Pattern...
...ure 11. Combined PPFE and UIP Patter...
...gure 12. Three of the Four High-resolution...
...13. PPF in a Patient With IPF (Probable U...
...e 14. PPF Due to NSIPA) CT in a 45 year...