Cystic Fibrosis Colorectal Cancer Screening

Publication Date: December 28, 2017
Last Updated: March 14, 2022

Recommendation Statements

The CF Foundation recommends that all decisions on colorectal cancer screening and surveillance in individuals with CF be based on shared decisions between the provider and individual with CF about: treatment, comorbidities, safety, and quality of life.
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The CF Foundation recommends that all colorectal cancer screening and surveillance for individuals with CF are jointly managed by CF health care professionals and an endoscopist.
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The CF Foundation recommends colonoscopy as the screening examination for CRC in individuals with CF.

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The CF Foundation concludes that the evidence is insufficient to recommend the use of computed tomography colonography, stool-based tests, or flexible sigmoidoscopy in individuals with CF for the purpose of CRC screening.
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The CF Foundation recommends that CRC screening begin at age 40 y in individuals with CF with continued rescreening every 5 y.
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The CF Foundation recommends that individuals with CF who have undergone a colonoscopy that had any adenomatous polyps have surveillance colonoscopy in 3 y, unless a shorter interval is indicated by individual findings, with subsequent intervals based on the most recent endoscopic examination.
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The CF Foundation recommends that individuals with CF who are 30 years of age and older and have adequately recovered after receiving a solid organ transplantation begin CRC screening within 2 years of transplantation, except when they have had a negative colonoscopy within the past 5 y.
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The CF Foundation recommends continued CRC rescreening every 5 y in individuals with CF who have received a solid organ transplant.
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The CF Foundation recommends that individuals with CF who have undergone a solid organ transplantation and had colonoscopy that had any adenomatous polyps have surveillance colonoscopy in 3 years, unless a shorter interval is indicated by individual findings, with subsequent intervals based on the most recent endoscopic examination.
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The CF Foundation recommends that adults with CF undergoing a colonoscopy receive intensive regimens for bowel preparation to allow for optimal examination. The intensive regimen should include: 3-4 washes (minimum of 1 L purgative per wash) with the last wash occurring within 4-6 h before the examination.
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Recommendation Grading

Overview

Title

Cystic Fibrosis Colorectal Cancer Screening

Authoring Organization

Cystic Fibrosis Foundation

Publication Month/Year

December 28, 2017

Last Updated Month/Year

August 7, 2023

Supplemental Implementation Tools

Document Type

Guideline

External Publication Status

Published

Country of Publication

US

Inclusion Criteria

Female, Male, Adolescent, Adult, Child, Infant

Health Care Settings

Hospital, Operating and recovery room, Outpatient

Intended Users

Social worker, epidemiology infection prevention, nurse, nurse practitioner, physician, physician assistant

Scope

Assessment and screening, Management

Diseases/Conditions (MeSH)

D015179 - Colorectal Neoplasms, D003550 - Cystic Fibrosis

Keywords

colorectal cancer, cystic fibrosis, colonoscopy, CFTR

Methodology

Number of Source Documents
51
Literature Search Start Date
February 1, 2016
Literature Search End Date
March 1, 2016