Metastatic Well-differentiated Gastroenteropancreatic Neuroendocrine Tumors

Publication Date: September 27, 2023

Key Points

Key Points

  • The focus of this guideline is advanced or metastatic well-differentiated G1-G3 gastroenteropancreatic neuroendocrine tumors (GEP-NETs), including tumors arising in sites such as the pancreas, stomach, small intestine, colon, rectum, and appendix.
    • These are classified according to mitotic rate or Ki-67 index (a measure of the percentage of primary tumor cells that are dividing).
  • This guideline focuses on strategies for controlling the growth of these tumors.

Treatment

...reatmen...

...eral Recommendations for G1–G3 GEP-NE...

...tion 1.1Selection of initial treatment opt...

...tion 1.2All treatment decisions should be g...

...endation 1.3Patients should be assess...


...mic Therapy for Metastatic G1–G2 Gas...

...stemic Therapy for G1–G2 GI-NETs...

...2.1SSAs (octreotide or lanreotide) are recom...

...2.2In the less common circumstance of patient...

...or Later-line Systemic Therapy for G1â...

...dation 2.3Peptide receptor radionu...

....4Everolimus is recommended for patients with non-...


...herapy for Metastatic G1–G2 Pancreati...

...t-line Systemic Therapy for G1–G2 panNETs

...mmendation 3.1SSAs (octreotide or lanreotide) a...

...commendation 3.2Chemotherapy (e.g....

...ion 3.3Chemotherapy (e.g., CAPTEM), everolimu...

...econd- or Later-line Systemic Therapy for...

....4PRRT for SSTR-positive tumors, che...


...temic Therapy for G3 GEP-NETs...

...ecommendation 4.1The range of systemic options o...


Table 1. WHO Classification and Gradi...


...gure 1. Systemic Therapy for Tumor C...


...s that cancer clinical trials are vital to inform...