Interstitial Lung Disease in People With Systemic Autoimmune Rheumatic Disease

Publication Date: July 8, 2024

Key Points

Key Points

Guideline Summary:

  • This guideline provides evidence-based recommendations for the screening and treatment of Interstitial Lung Disease (ILD) in people with Systemic Autoimmune Rheumatic Diseases (SARDs) (Rheumatoid Arthritis [RA], Systemic Sclerosis [SSc], Idiopathic Inflammatory Myositis [IIM including polymyositis, dermatomyositis, antisynthetase syndrome, immune-mediated necrotizing myopathy], Mixed Connective Tissue Disease [MCTD], and Sjögren’s Disease [SjD]) associated with the greatest risk of ILD, and for monitoring for ILD progression.

Screening and Monitoring

...reening and Moni...

...le 2. Risk Factors for the Developme...


...ary of Recommendations for Screening of S...

...commendations...

...r people with SARDsa at increased risk of develo...

...le with SARDs at increased risk of deve...

...h SARDs at increased risk of developing ILD,...

...or people with SARDs at increased risk of develo...

...r people with SARDs at increased risk...

...SARDs at increased risk of developing ILD, we c...

...r people with SARDs at increased risk of dev...

...r people with SARDs at increased risk of developin...


...4. Summary of Recommendations for Mo...

Recommendation...

For people with SARDs-ILD, we conditionally recom...

...th SARDs-ILD, we conditionally recommend monit...

...e with SARDs-ILD, we conditionally re...

...SARDs-ILD, we conditionally recommend monitorin...

...people with SARDs-ILD, we conditionally re...

...ople with SARDs-ILD, we conditionally recomme...

...SARDs-ILD, we conditionally recommend aga...

For people with IIM-ILD and SSc-ILD, we suggest P...

...people with RA-ILD, SjD-ILD, and MCTD...

...ple with SARDs-ILD, we do not provide guidance...

...SARDs-ILD, we suggest assessment for am...


...mmendations for ILD Screening and MonitoringNote:...


.... Interstitial Lung Disease Screening and Monit...


Treatment

...atment

...ummary of Recommendations for Mana...

...ecommendat...

...ple with SARD-ILD other than SSc-ILD, we co...

...people with SSc-ILD, we strongly reco...

...people with SARD-ILD, we conditionally recommend m...

...SSc-ILD and MCTD-ILD, we conditio...

...with SARD-ILD, we conditionally recom...

...le with SSc-ILD, we conditionally recommend nint...

...ple with SjD-ILD, IIM-ILD, and MCTD-ILD, we co...

...le with RA-ILD, the Panel was not able to come...

...people with SARD-ILD, we conditionally r...

...r people with SARD-ILD receiving mycophenolate wit...

...e with SARD-ILD, we conditionally...

...ith IIM-ILD, we conditionally recommend JAK inh...

...with SARD-ILD other than IIM-ILD, we c...

...with IIM-ILD, we conditionally recom...

...or people with SARD-ILD other than IIM-ILD,...

...SARD-ILD, we conditionally recommend...

...or people with SARD-associated ILD, we conditional...


...commendations for Management of SARD-ILD P...

...mendations...

...e strongly recommend against using long-term g...

...r SARD-ILD we conditionally recommend agains...

...SARD-ILD progression despite first ILD trea...

...or people with RA-ILD progression despite first...

...th SARD-ILD, other than RA-ILD, progression despi...

...e with SSc-ILD, MCTD-ILD, RA-ILD progression de...

...with SjD-ILD and IIM-ILD progressi...

...IIM-ILD progression despite first ILD treat...

...with SARD-ILD, other than IIM-ILD, prog...

...IIM-ILD progression despite first ILD tr...

...eople with IIM-ILD and MCTD-ILD progressio...

...ople with SARD-ILD progression despite first...

...ple with SSc-ILD progression despi...


...e 3. Initital Treatment Options for the Treatmen...


...endations for Management of SARD-ILD Progre...


...endations for Management of SARD With R...

...ecommendations...

...th SARD and RP-ILD, we conditionally recomm...

...with SARD and RP-ILD, we conditionally reco...

...with SARD and RP-ILD, we conditionally recommend...

...people with RP-ILD, we conditionally recom...

...le with SARD and RP-ILD, we conditionally reco...

...th SARD and RP-ILD, we conditionally recom...


.... Recommendations for Management of SARD...