Title
Health Supervision for Children and Adolescents With Sickle Cell Disease
Authoring Organization
Publication Month/Year
July 22, 2024
Last Updated Month/Year
July 23, 2024
Supplemental Implementation Tools
Document Type
Consensus
Country of Publication
US
Document Objectives
Sickle cell disease (SCD) is a group of complex genetic disorders of hemoglobin with multisystem manifestations. The scope of this clinical report is such that in-depth recommendations for management of all complications is not possible. Rather, the authors present an overview focused on the practical management of children and adolescents with SCD and the complications that are of particular relevance to pediatric primary care providers. References with detailed commentary provide further information. Timely and appropriate treatment of acute illness is critical, because life-threatening complications may develop rapidly. Specialized comprehensive medical care decreases morbidity and mortality during childhood. The provision of comprehensive care is a time-intensive endeavor that includes ongoing patient and family education, periodic comprehensive evaluations and other disease-specific health maintenance services, nursing support, psychosocial care, and genetic counseling. Ideally, this care includes comanagement by the pediatrician or other pediatric primary care provider and a team of specialist SCD experts: Hematologist, other pediatric specialists, advanced practice providers, nurse specialists, social workers, patient navigators, and educational liaisons.
Target Patient Population
Children and adolescents with sickle cell disease
Target Provider Population
Pediatricians, hematologists, and allied providers caring for children and adolescents with sickle cell disease
Inclusion Criteria
Male, Female, Adolescent, Child, Infant
Health Care Settings
Ambulatory, Outpatient
Intended Users
Nurse, nurse practitioner, physician, physician assistant
Scope
Management
Diseases/Conditions (MeSH)
D000755 - Anemia, Sickle Cell
Keywords
sickle cell disease, Sickle Cell, acute chest syndrome, erythrocyte transfusion, sickle cell anemia
Source Citation
Amber M. Yates, Banu Aygun, Rachelle Nuss, Zora R. Rogers, Section on Hematology/Oncology, AMERICAN SOCIETY OF PEDIATRIC HEMATOLOGY/ONCOLOGY; Health Supervision for Children and Adolescents With Sickle Cell Disease: Clinical Report. Pediatrics 2024; e2024066842. 10.1542/peds.2024-066842