Cystic Fibrosis Evidence-Based Nutrition Recommendations

Publication Date: February 1, 2020

Introduction

Introduction

Cystic fibrosis (CF) is a genetic disease in which affected individuals produce thick, sticky mucus in multiple organs, including the lungs and pancreas. The complexity of this disease requires an interdisciplinary, integrated approach to care. Nutrition care is central to this approach, since poor nutritional status in individuals with CF is associated with disease decline. Nutritional status is likely to be compromised in individuals with CF, because CF increases energy needs as well as nutrient malabsorption.

Screening and Referral

...ng and Referral

...: Frequency of Nutrition Screening, Less Than...


...ethod of Nutrition Screening, Less Than 2 Y...


...F: Frequency of Nutrition Screening, 2-20 Years...


...hod of Nutrition Screening, 2-20 Years of Age Pe...


...requency of Nutrition Screening, Adults In adult...


...f Nutrition Screening, Adults Adults with CF grea...


Nutrition Assessment

...trition Assessment...

...y of Nutrition Assessment In individu...


...n Assessment Components In individuals with C...


...odulators in Nutrition AssessmentÂ...


...alorimetry In pediatric (≤20 years of age) and...


...stimating Energy Needs, Pediatrics In pediatric...


...ating Energy Needs, Adults In adu...


...y X-Ray Absorptiometry (DEXA) In individuals...


...ngle-Site Anthropometric Measures and Nutritio...


...curacy of Skinfold Measures and Bioelectrical I...


...Tolerance Testing (OGTT) For individuals...


...ble Vitamins For all individuals...


...Lipid Profile For individuals with...


Nutrition Intervention

...utrition Intervention

...Approach RDNs or international equ...


...ll-Time Equivalents (FTEs) It is reasonable...


...plement Intake For all individuals with CF, it is...


...terns For all individuals with CF, it is re...


CF: Meal and Snack Frequency For all indi...


...Intake with CF-Related Diabetes For all...


...ake with Overweight/Obesity For individuals with...


...: Macronutrient Distribution For...


...ber Intake For individuals with CF, the RDN o...


...nt Feeding In infants diagnosed with CF, the RD...


Nutrition Monitoring and Evaluation 

...tion Monitoring and Evaluation ...